1.
Article
in English
| IMSEAR
| ID: sea-65546
2.
Article
in English
| IMSEAR
| ID: sea-64156
ABSTRACT
Hereditary angioedema is a rare disorder characterized by quantitative or qualitative deficiency of complement C1 esterase inhibitor. We report a family whose members presented with recurrent angioedema and abdominal pain; the diagnosis was confirmed by quantitative assay of C1 inhibitor. The index patient was treated with danazol and was relieved.